Please use this identifier to cite or link to this item:
PIRA download icon_1.1View/Download Full Text
DC FieldValueLanguage
dc.contributorSchool of Optometryen_US
dc.creatorChoi, KYen_US
dc.creatorWong, HHYen_US
dc.publisherLippincott Williams & Wilkinsen_US
dc.rights© 2021 American Academy of Optometryen_US
dc.rightsThis is a non-final version of an article published in final form in Choi, Kai Yip, Wong, Horace Ho Yin, Chan, Henry Ho Lung. Utilizing Advanced Technology to Facilitate Diagnosis of Rare Retinal Disorders: A Case of Bietti Crystalline Dystrophy. Optometry and Vision Science 98(9):p 1031-1038, September 2021. DOI: 10.1097/OPX.0000000000001763. Optometry and Vision Science is available at
dc.titleUtilizing advanced technology to facilitate diagnosis of rare retinal disorders : a case of Bietti crystalline dystrophyen_US
dc.typeJournal/Magazine Articleen_US
dcterms.abstractSIGNIFICANCE: Optometrists, as primary eye care providers, encounter patients with rare ocular disease such as Bietti crystalline dystrophy from time to time. Using advanced technologies, which are also useful in managing common ocular conditions, to facilitate a prompt diagnosis is highly recommended.en_US
dcterms.abstractPURPOSE: This report describes a patient with clinically diagnosed Bietti crystalline dystrophy with findings on funduscopy, multimodal imaging, and visual electrophysiology.en_US
dcterms.abstractCASE REPORT: A 41-year-old Chinese woman who had subjectively progressing dimmed vision (especially in the left eye) for 9 months was referred to our clinic to test for retinitis pigmentosa. Best-corrected visual acuities were 6/6 and 6/7.6 in the right and left eyes, respectively. Funduscopy revealed multiple crystalline deposits on the posterior pole in both eyes. The 30-2 perimetry displayed bi-inferotemporal scotoma (left > right eye). Scotopic flash electroretinogram (ERG) yielded a normal result, whereas photopic ERG was slightly attenuated. Electro-oculogram showed an abnormal adaptation time course of the retinal pigmented epithelium (RPE). Multifocal ERG revealed a decreased central retinal response, but paracentral responses were relatively better preserved. Optical coherence tomography showed multiple patches of RPE atrophy, with disruption of the left ellipsoid zone. Outer retinal tubulations, hyperreflective dots on RPE–Bruch's membrane interface, and intraretinal bright spots were also identified.en_US
dcterms.abstractCONCLUSIONS: Rare ocular diseases like Bietti crystalline dystrophy can be encountered by optometrists. This case report shows the ophthalmic findings of a rare chorioretinal dystrophy and provides insight on how to better use advanced equipment in an optometric practice to facilitate prompt diagnoses.en_US
dcterms.accessRightsopen accessen_US
dcterms.bibliographicCitationOptometry and vision science, Sept 2021, v. 98, no. 9, p. 1031-1038en_US
dcterms.isPartOfOptometry and vision scienceen_US
dc.description.validate202109 bcvcen_US
dc.description.oaAccepted Manuscripten_US
dc.description.fundingTextThe Innovation & Technology Fund and the Government of the Hong Kong Special Administrative Region.en_US
Appears in Collections:Journal/Magazine Article
Files in This Item:
File Description SizeFormat 
Choi_Utilizing_Advanced_Technology.pdfPre-Published version1.57 MBAdobe PDFView/Open
Open Access Information
Status open access
File Version Final Accepted Manuscript
View full-text via PolyU eLinks SFX Query
Show simple item record

Page views

Last Week
Last month
Citations as of Oct 1, 2023


Citations as of Oct 1, 2023

Google ScholarTM



Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.